PDSS2( Human )

Entrez Gene 57107 Entrez Gene 57107
decaprenyl diphosphate synthase subunit 2

Alias

C6orf210|COQ10D3|DLP1|bA59I9.3|hDLP1

The protein encoded by this gene is an enzyme that synthesizes the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. Defects in this gene are a cause of coenzyme Q10 deficiency.[provided by RefSeq, Oct 2009].

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